Juvenile pemphigus is a rare disease with similar course as pemphigus in adulthood. It begins as stomatitis followed by skin disease. Its diagnosis may be delayed for several months. A case of severe juvenile pemphigus in a 13-year-old girl with a 4-year follow up is described. The patient was treated with corticosteroids, dapsone, azathioprine and intravenous immunoglobulins. The treat- ment was complicated with serious adverse effects of corticosteroids.

        Key words: pemphigus vulgaris - juvenile - treatment