Advances in pathophysiological knowledge, and in particular results of molecular biology, made its possible to assemble recently new findings on Bartter’s syndrome. At present the view is generally accepted that this tubulopathy is not unique but that it is a heterogeneous group of diseases associated with impaired renal electrolyte transport. This is also the reason for the changing terminology of this tubular dysfunction. The term used recently in clinical practice is „Bartter-like syndromes“. The submitted paper presents a review on modern findings pertaining to this nephropathy, the terminology of which may be yet altered in future on the basis of new analyses of nephrologically oriented molecular biology which may extend the hitherto known spectrum of four genes coding electrolyte transport in distal portions of the nephron by the discovery of new ones.

        Key words: Bartter’s syndrome, Bartter-like syndromes, tubulopathy