Aspects of Psychological Care of Patients with Phenylketonuria
Vaďurová L.1, Šťastná S.1, Hyánek J.1,2
Ústav dědičných metabolických poruch VFN a 1. LF UK, Praha1 přednosta prof. MUDr. M. Elleder, DrSc. Oddělení klinické biochemie, hematologie a imunologie, Nemocnice Na Homolce, Praha2 primář prof. MUDr. J. Hyánek, DrSc. |
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Summary:
Psychological care is the necessary part of complex lifetime care of patients with phenylketonuria/hyperphenylalaninemia
(PKU/HPA). The aim of the article is to summarize long-time experience of the clinical psychologist
with care of the group of 14 women with PKU/HPA in the critical periods of their life, with emphasis on the period
of preconception care and pregnancy. Superior psychological care improves dietary compliance of patients with
PKU/HPA and reduces risk of phenylalanine embryopathy or fetopathy in embryo and fetus.
Key words:
phenylketonuria, hyperphenylalaninemia, psychology, anxiety, compliance
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