Presented article deals with the pathogenesis of cryptogenic fibrotizing alveolitis (CFA), gives distinct
histological types according ATS and ERS, considers clinical CFA picture and recommends examination
program for this disease. The anti-inflammatory and immunosuppressive treatment is discussed together
with other therapeutic approaches (long-lasting oxygenotherapy at home, transplantation and treatment
of pulmonary hypertension). Final part deals with less frequent clinical manifestations.
cryptogenic fibrotizing alveolitis, pathogenesis, diagnostics, treatment.