Dermatomyositis represents a progressive autoimmune disease of the connective tissue with SLE-like dermatitis,
with inflammatory myopathy and muscular weakness. It is an infrequent and serious disease affecting not only the
skin and striatedmuscle. Caseswithout skin affection are classified as polymyositis. Beside autoimmune mechanisms,
aetiology includes also genetic, environmental and paraneoplastic factors. Clinical skin symptoms as well as
histopathological findings include Gottron’s papulae, heliotropic periorbital erythrema, which, together with
palpebral oedema, brings about the weepy look of patients. None of these signs is pathognomic and beside the
cutaneous symptoms the diagnosis requires 3out of 4other diagnostic criteria for the muscle symptoms. Cutaneous
symptoms can precede myositis with various time intervals; such situation is sometimes classified as Amyopathic
dermatomyositis (ADM), dermatitis sinemyositis or skin dermatomyositis.Acase of anADMpatient and the analysis
of problematic including the strategy of therapy are presented.
dermatomyositis, amyopathic form, therapy.