Acquired auditory disorders in children have different causes. They can be stationary or progressive. Only some which developed suddenly are reversible if they are immediately treated by peripheral vasodilatating agents. Fluctuating auditory disorders of the inner ear are little known in children and frequently develop into a progressive severe auditory disorder. In the submitted case-history the authors draw attention to a case of rare fluctuating auditory disorder in a four-year-old child caused by autoimmune disease. By detection of the cause (autoimmune disease) and corticoid treatment not only deafness was prevented but also damage of other organs caused by the autoimmune disease.

        Key words: fluctuating hearing disorder of the inner ear, children, autoimmune disease.