Tumoriform Tracheal Amyloidosis
Jirmanová I., Šťastný B., Marel M., Haškovcová I. 1
Pneumologická klinika 1. LF UK Praha, přednosta doc. MUDr. Boris Šťastný, CSc., 1 Patologicko-anatomický ústav 1. LF UK Praha, přednosta prof. MUDr. Ctibor Povýšil, DrSc. |
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Summary:
Tracheobronchial amyloidosis is the rare disease of respiratory tract. The etiology is unknown, the disease is
characterized by the deposition of amyloid, heterogeneous
protein and saccharide, in the submucosa of respiratory
tract. That depositions narrow the respiratory airways
with produce endotracheal and endobronchial tubercules
or deformations. The authors discuss etiopathogenesis,
forms and classification of amyloidosis, in detail they
analyse amyloidosis of respiratory tract. A case of a female patient with tumoriform tracheal amyloidosis is reported.
Key words:
amyloidosis, tracheobronchial amyloidosis,
bronchoscopy, endoscopi canalization
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