Acute vasculitis of medium arteries – Kawasaki disease – is not a rare illness even in our geographical conditions, although it clearly predominates in the Japanese population. In most cases there is a spontaneous decline in clinical picture symptoms, but without any therapeutic intervention the disease represents a 20 – 25% risk of affected coronary arteries with acute and chronic consequences. The administration of high doses of immunoglobulins is clearly a method of choice, which significantly decreases the risk. The diagnostic pitfalls represent incomplete forms, especially in infants. In this age there is a greater risk of coronary lesions.

        Key words: Kawasaki disease, incomplete forms, coronary aneurysms, intravenous immunoglobulins