5–20% paragangliomas originates from extraadrenal tissue paralelly to occurrence of anatomic components of vegetative nervous system. This distribution corresponds to embryological development of paraganglias from cells of neural crest. This tumors can extraordinary rise also except this usual area. Case report of patient whose paraganglioma was detected in the mesenterium but suggested to be a lymphoma due to enlarged lymfatic nodules and Epstein-Barr virus and cytomegalovirus reactivation has been presented. This extremely unusual paragangliom locality was described only in four cases till now. A normal neurovegetative tissue of paraganglioma occurs only around mesenteric artery branching. Hypothetically speaking the explanation for paraganglioma in mesenterium seems to be a consequence of the migration of neural crest cells ventrally around this vessels. Case report describes differential diagnostic consideration and also unusual pseudotumorous reaction to foreing body material by desmoid proliferation which complicated surgery. The aim of the paper is to stress the possibility of unusual localisation of paragalioma and differential diagnostic consideration during the course of described ilness.

        Key words: paraganglioma – differential diagnostic – unusual localisation