Summary:
On the case of a patient who had medical care on account of a febrile disease diagnosed as
pleuritis the authors draw attention to a relatively new pathological unit described as the „Bruga-
da syndrome“. It is a genetically conditioned anomaly of sodium channels, which, when fully
expressed, is manifested by a picture resembling right bundle branch block, elevation of ST
segment in leads V1 - V3 and the occurrence of malignant ventricular arrhythmias or sudden
death without structural heart disease. Neither the reported patient nor his family suffered from
arrhythmias. The authors present however a typical
electrocardiographic picture ad positive test with ajmaline, a substance which by blocking sodium channels can frequently induce latent and variable changes.
Key words:
Brugada syndrome - Sudden death - Right bundle branch block - Segment elevation
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