The author submits information on Stargardt´s disease, and based on a case-report he mentions actual steps which led to the establishment of the diagnosis of the disease. Stargardt´s disease is one of the forms of juvenile macular degeneration which affects the retinal pigmented epithelium. It is a relatively rare hereditary, slowly progressing, usually bilateral disease leading to deterioration of vision. In the majority the heredity is autosomal recessive. The majority of ophthalmologists do not encounter the disease in their practice but it has to be taken into consideraction.

        Key words: Stargardt´s disease, juvenile macular degeneration, autosomal reces- sive heredity