Common cause of sudden death in children and teenagers are primary cardiomyopathies, mostly hypertrophic. The authors refer to arrhythmogenic right ventricular dysplasia / cardiomyopathy as a possible cause of sudden death. The disease is not limited to the right hearth only, the presence of fat and scar tissue in the in the hearth muscle is variable.

        Key words: sudden cardiac death – arrhythmogenic right ventricular dysplasia / cardiomyopathy, ARVD/C