The group of patients with the Marfan syndrome is used to suffer from aneurysm and dilatation of the ascendent aorta, therefore the reason echocardiografy examination is necessary. But in spite of this, although the dimensions (measures) are stable, we do really not know when the dissection appeare. This complication is the most usual cause of death these patients. But if we recognize the diagnosis in time and if we treat it correctly, this complication can be treated with the great difference in mortality. That is while we must think of this possible complication in case of atypical breast ache. The following case describes the acute dissection of the aorta in the proximal and also descendent part together with the acute aortal significant regurgitation and the volume overload of the left chamber appeared on female - patient with the Marfan syndrome.

        Key words: Marfan syndrom - Aortic dilatation - Acute dissection of the aorta